Agenesis of left upper lobe of lung

Agenesis of left upper lobe of lung is very rare and may remain undiagnosed for many years. Lobar agenesis is usually asymptomatic but symptoms may occur if the main bronchus is displaced upwards due to volume loss created by lobar agenesis causing improper drainage of respiratory secretions. We report chronic recurrent cough in a 34-year-old male as an unusual presentation of agenesis of left upper lobe. The left upper lobe was not visualized through computed tomography (CT) of chest. Patent foramen ovale and patent ductus arteriosus were also detected as co-incidental cardiac anomalies. Whenever congenital malformations of lung is suspected, CT of chest is recommended before other invasive procedures like pulmonary angiography is considered.