Alveolar rhabdomyosarcoma of paranasal sinus with cervical metastasis - A case report

Rhabdomyosarcoma (RMS) is a rare tumour in adults and involvement of paranasal sinuses is extremely rare comprising only 1.5% of reported head and neck rhabdomyosarcomas. Alveolar type, a rare form of RMS, mainly seen in adults, has the worst prognosis. Incidence of lymph node metastases is more common in this type, compared to the other forms. An aggressive combined modality of treatment has dramatically improved the poor survival statistics noted previously. Our experience with one such case occurring in paranasal sinus and orbit which was managed by surgery, multidrug chemotherapy and radical radiotherapy is discussed and relevant literature has been reviewed.