Anaesthetic management of a neonate with congenital pulmonary airway malformation for pneumonectomy – A case report

Congenital pulmonary airway malformations (CPAM) are rare bronchopulmonary developmental disorders with cystic lesions [1]. It is because of embryonic insult before 50th day of gestation [2]. These cystic lesions do not take part in gas exchange. Anaesthetic management is quite challenging due to the risk of rupture of these cysts, pneumothorax, cardiovascular collapse. Prognosis of these cases depends on the size of the lesion, hypoplasia of the remaining lung. We present a case of a 4-day old neonate diagnosed with macrocystic CPAM antenatally who underwent thoracotomy and partial pneumonectomy in a resource limited setup. Such cases can be managed in low resource setting, and this report will encourage other anaesthesiologists in managing high risk cases.