TY - JOUR
T1 - Imaging of leiomyomas arising from Müllerian remnants in a case of Mayer-Rokitansky-Küster-Hauser syndrome
AU - Narayanan, Ramakrishna
AU - Mariappan, Supritha
AU - Paulraj, Santhanakumar
AU - Shankar, Balasubramanyam
N1 - Publisher Copyright:
© 2015 Babaeian et al.
PY - 2015/10/1
Y1 - 2015/10/1
N2 - Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital abnormality characterised by varying degrees of aplasia or hypoplasia of the uterus and vagina. Very rarely, leiomyomas or adenomyosis can develop in the Müllerian remnant tissue or rudimentary uterus. We present a case of a 43-year-old woman with MRKH syndrome, who presented with primary amenorrhoea and lower abdominal pain. On examination, a large pelvic mass was palpated and a provisional diagnosis of ovarian tumour was made. MRI showed multiple large leiomyomas arising from the Müllerian remnant tissue, and chronic torsion of the right ovary.
AB - Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital abnormality characterised by varying degrees of aplasia or hypoplasia of the uterus and vagina. Very rarely, leiomyomas or adenomyosis can develop in the Müllerian remnant tissue or rudimentary uterus. We present a case of a 43-year-old woman with MRKH syndrome, who presented with primary amenorrhoea and lower abdominal pain. On examination, a large pelvic mass was palpated and a provisional diagnosis of ovarian tumour was made. MRI showed multiple large leiomyomas arising from the Müllerian remnant tissue, and chronic torsion of the right ovary.
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U2 - 10.1136/bcr-2015-210737
DO - 10.1136/bcr-2015-210737
M3 - Article
C2 - 26430230
AN - SCOPUS:84945906059
SN - 1757-790X
VL - 2015
JO - BMJ Case Reports
JF - BMJ Case Reports
M1 - A1522
ER -