Maxillofacial rehabilitation of lamellar ichthyosis

Lamellar ichthyosis (LI) is a rare genetic skin disorder that is present at birth, with an incidence of <1:300,000 in different parts of the world. However, there is little evidence of oral manifestations. Oral symptoms and oral rehabilitation of this condition are mostly unknown. This case report reiterates the need for proper dental diagnosis, treatment planning, and follow-up for a holistic approach. Here, we describe the oral manifestations and successful complete oral rehabilitation procedure performed in a 19-year-old female patient who had prediagnosed LI with skeletal class III jaw discrepancy due to maxillary deficiency.